Dyke Davidoff Masson syndrome (DDMS) is characterized by seizures, facial 
asymmetry, contralateral hemiplegia and mental retardation. The characteristic 
radiologic features are cerebral hemiatrophy with homolateral hypertrophy of the 
skull and sinuses. We report a case of DDMS in an 18-month-old girl who 
presented with right sided focal seizures, hemiparesis of the same side, and 
delayed milestones.