Dyke-Davidoff-Masson syndrome is a condition characterized by seizures, facial 
asymmetry, contralateral hemiplegia or hemiparesis and mental retardation. We 
report the clinical and imaging features in two patients with epilepsy revealing 
a Dyke-Davidoff-Masson syndrome. Brain MRI showed unilateral loss of cerebral 
volume with hypertrophy and hyperpneumatization of the paranasal sinuses and 
mastoid cells. Ipsilateral fronto-parietal polymicrogyria was present in one 
patient.