The coincidence of hemolysis, elevated liver enzymes, and low platelet count 
(HELLP) syndrome and cortical blindness is an uncommon but very dramatic event. 
We describe a case of HELLP syndrome complicating with acute cortical blindness 
before delivery. A 27 year-old woman, gravida 1, para 0, with normal medical 
history, was referred to our emergency department at the 33th week of gestation 
due to headache, vomiting, and blurred vision. The ophthalmologic examination 
showed intact pupillary light reflexes and normal ophthalmoscopic findings, but 
no light perception in either eye. Brain computed tomography showed normal 
findings. HELLP syndrome and preeclampsia was diagnosed based on the findings of 
hypertension and proteinuria as well as laboratory data. Prompt delivery was 
performed in order to achieve good maternal and neonatal outcomes.