Bartter's syndrome is an autosomal recessive renal tubular disorder 
characterized by hypokalemia, hypochloremia, metabolic alkalosis, and 
hyperreninemia with normal blood pressure. Bartter's syndrome is associated with 
hypercalciuria and nephrocalcinosis. Amelogenesis imperfecta (AI) is a group of 
hereditary disorders that affect dental enamel. AI could be part of several 
syndromes. The enamel renal syndrome is the association of AI and 
nephrocalcinosis. We report two patients of AI with Bartter's syndrome.