Kartagener's syndrome is a very rare congenital malformation comprising of a 
classic triad of sinusitis, situs inversus and bronchiectasis. Primary ciliary 
dyskinesia is a genetic disorder with manifestations present from early life and 
this distinguishes it from acquired mucociliary disorders. Approximately one 
half of patients with primary ciliary dyskinesia have situs inversus and, thus 
are having Kartagener syndrome. We present a case of 12 year old boy with 
sinusitis, situs inversus and bronchiectasis. The correct diagnosis of this rare 
congenital autosomal recessive disorder in early life is important in the 
overall prognosis of the syndrome, as many of the complications can be prevented 
if timely management is instituted, as was done in this in this case.