The Ehlers-Danlos Syndrome (EDS) is a rare connective tissue disorder 
characterised by fragility of the soft connective tissues and widespread 
manifestations in skin, ligaments, joints, blood vessels and internal organs. We 
report a case of a 12-year-old boy, previously diagnosed with 
kyphoscoliosis-type EDS (type VI), presenting with a left brachial artery 
pseudo-aneursym with history of multiple spontaneous and post-traumatic arterial 
ruptures. Surgical management of this patient was performed successfully by 
primary repair of brachial artery lesion.