Pseudotumor cerebri is a clinical syndrome characterized by raised intracranial 
pressure with normal ventricular size, anatomy and position. Headache, vomiting 
and diplopia are the most common symptoms. Signs include those of raised 
intracranial pressure including papilledema and absence of focal neurological 
signs. A secondary cause is identifiable in 50% of children; the most common 
predisposing conditions are otitis media, viral infection and medications. 
Management is mainly directed towards identifying and treating the cause and 
measures to reduce the raised intracranial pressure. Though it is mostly a self 
limited condition, optic atrophy and blindness can occur. Oculomotor nerve palsy 
is very rarely associated with pseudotumor cerebri. We report a unique case of 
pseudotumor cerebri who had left Oculomotor palsy with sparing of the pupillary 
fibres, which resolved following treatment with oral acetazolamide.