Hemophilic pseudotumor is a rare complication of hemophilia. We present the case 
of a male toddler with moderate hemophilia A and cranial hemophilic pseudotumor 
managed with factor VIII infusions. We also provide a review of the literature. 
Recognition of this rare manifestation of this complication of hemophilia is 
important to provide correct treatment and avoid unnecessary investigations, 
particularly biopsy, which is contraindicated in this condition.