We report on the effects of bilateral neurostimulation of the ventral 
intermediate thalamic nucleus (VIM) in a patient with medically intractable and 
progressing inherited myoclonus dystonia syndrome (IMDS). Postoperatively, the 
patient improved by approximately 80% on the modified version of a myoclonus 
score without any significant change in the dystonic symptoms. This suggests 
that neurostimulation of the VIM may be an effective treatment for myoclonus in 
pharmacologically intractable IMDS.