Behçet disease (BD) is a rare relapsing, multisystem vasculitis characterised by 
recurrent oral and genital ulcers, and uveitis. As an autoimmune small vessel 
vasculitis, BD can involve other organs including the skin, joints, nervous 
system, kidney and the gastrointestinal tract. This report describes a 
40-year-old woman who presented with an uncommon feature of BD, namely myositis, 
and who went on to develop myocarditis and polymicrobial necrotising fasciitis. 
To the best of our knowledge, this is the first reported case of an 
immunocompromised-associated infection occurring in BD without concurrent 
immunosuppressive therapy.