Bobble-head Doll Syndrome is a rare and unique movement disorder found in 
children. Clinically, it is characterized by a to and fro or side to side 
movement of the head at the frequency of 2 to 3 Hz. It is mostly associated with 
cystic lesions around the third ventricle, choroid plexus papilloma, aqueductal 
stenosis and other rare disorders. An eleven year old child presented in the 
outpatient department with continuous to and fro movement of the head and 
declining vision for the last one month. MRI Scan showed a large 
contrast-enhanced lesion in the region of the third ventricle along with gross 
hydrocephalus. Ventriculo-peritoneal shunt was inserted and the movements of the 
head disappeared completely. Bobble-head doll syndrome is a rare condition and 
therefore this case is presented and the literature reviewed.