Sturge-Weber syndrome is a disorder characterized by ipsilateral cavernous 
hemangioma of the face, uvea, and brain in patients who may present with an 
enlarged eye, exudative retinal detachment, glaucoma, and seizures. This report 
presents the clinicopathologic findings of an otherwise healthy infant with 
ipsilateral arteriovenous and capillary hemangiomas of the face and uveal tract, 
microphthalmos, iris heterochromia, hypotony, and absence of central nervous 
system involvement. The association of an arteriovenous-capillary angioma of the 
ocular adnexa and ipsilateral uveal tract is a syndrome that is distinct from 
Sturge-Weber syndrome.