Congenital generalized hypertrichosis associated with gingival hyperplasia are 
rare cases published in literature. The frequency incidence of generalized 
congenital hypertrichosis is about one to billions of people. Hypertrichosis and 
gingival hyperplasia are termed as Ambras syndrome (AS), which can be noticed at 
birth or soon after. Here, is a rare case report of 4-year-old male child who 
presented with generalized hypertrichosis with gingival fibromatosis and 
dysmorphic facial features.