Tuberous sclerosis (TSC) is an autosomal-dominant genetic disease characterized 
by a spectrum of pathologic manifestations involving skin, brain, kidney, and 
heart. These manifestations include neuroectodermal, mesodermal, and skin 
lesions as well as a variety of associated tumors and hamartomas. We report an 
11-year-old male with previously diagnosed TSC who presented with a laryngeal 
mass shown on histology to be fetal cellular rhabdomyoma. Cardiac rhabdomyomas 
are common in TSC patients, but to our knowledge, the association between TSC 
and extracardiac rhabdomyomas has not been previously reported.