Ventricular noncompaction (VNC) of the myocardium is a rare genetic 
cardiomyopathy caused by a disorder during endocardial morphogenesis and could 
be accompanied by life-threatening complications. The major clinical 
manifestations of VNC are heart failure, arrhythmias, and embolic events. The 
left ventricle is the most commonly reported affected site, but a few cases of 
right ventricular involvement have also been reported. We report a case of 
biventricular noncompaction cardiomyopathy in a 31-year-old woman presenting 
with a new onset seizure. On the second day of her telemetry-monitored 
hospitalization, she suffered a witnessed ventricular fibrillation arrest 
requiring emergency direct-current cardioversion and induced hypothermia. 
Transthoracic echocardiography (TTE) showed isolated left ventricular (LV) 
noncompaction and depressed LV systolic function. Subsequent cardiac magnetic 
resonance imaging (MRI) revealed both left and right ventricular noncompaction. 
This unusual presentation highlights the importance of a complete and thorough 
evaluation of patients even when presenting with apparently noncardiac 
symptom(s).