An 88-year-old woman presented with fever and acute posterior neck pain. A CT 
scan revealed calcification of the transverse ligament and crown-like 
calcification around the odontoid process. According to the clinical and 
radiological findings, she was diagnosed with crowned dens syndrome (CDS). Her 
symptoms drastically improved following treatment with oral nonsteroidal 
anti-inflammatory medication. An X-ray of her wrist, elbow, shoulder and knee 
joints showed asymptomatic calcium deposits, suggesting underlying crystalline 
deposition disease. CDS may occur as the initial presentation of crystalline 
deposition disease. The measurement of procalcitonin and an X-ray survey of the 
major joints may be helpful for the diagnosis of CDS.