We report on a 12-year-old patient with Turcot Syndrome (Glioma polyposis). This 
patient's case deals with the association between a glioblastoma, anaplastic 
glioma (WHO Grade III) and colonic adenocarcinoma based on familial polyposis 
coli. Possible etiology and neurosurgical, clinically important characteristics 
of this rare syndrome, such as the young age of the patient and the relatively 
long survival time, will be discussed.