The Ehlers-Danlos syndromes (EDS) are a group of connective tissue disorders 
characterized by triad of joint hypermobility, skin extensibility, and tissue 
fragility. Ehlers-Danlos syndrome type IV places patients at risk for 
life-threatening, spontaneous, vascular or visceral rupture due to reduced or 
abnormal secretion of type III collagen. We present an adolescent male who was 
found to have a perisigmoid abscess with a fistula connecting to adjacent 
sigmoid colon secondary to undiagnosed EDS type IV. Conservative management with 
antibiotics and bowel rest was pursued to allow for elective resection for his 
acute complicated diverticulitis at a safer time.