AIM: The aim of this study is to establish the nature (urgent vs. non-urgent), 
demographics, presentation and management of Achenbach's syndrome and to 
formulate an algorithmic approach for their diagnosis and management.
MATERIALS AND METHODS: A systematic review and met-aggregation of literature 
from 1944 to 2015 in English language in MedLine, Embase and Cochrane database 
were conducted.
RESULTS: Achenbach's syndrome is a female-dominant disease with median age of 
49.5 years (range 22-76) (age ≤60, n = 11/12, 91 %). It presents with unilateral 
volar discoloration of a finger (100 %). It is associated with pain (n = 7/12, 
58. %), edema (n = 7/12, 58 %), and paresthesia (n = 3/12, 25 %). The median 
time to resolution of symptoms without any intervention was 4 days (range 2-14).
CONCLUSION: AS is self-limiting and a non-urgent surgical condition. It can be 
differentiated from other pathologies by clinical spectrum, patient demographics 
and in doubtful circumstances (acute limb ischemia) by Doppler sonography. An 
algorithmic approach can avoid hospital admissions, partially unnecessary 
investigation and assist in patient assurance.