A family with the Romano-Ward syndrome is presented. This family showed typical 
features of this syndrome with QT prolongation, torsades de pointes ventricular 
tachycardia, sudden death and an autosomal dominant inheritance pattern. The 
index case presented with an exacerbation of torsades de pointes ventricular 
tachycardia from diuretic induced hypokalaemia, and responded to diuretic 
withdrawal and beta blocker therapy.