Tay syndrome or IBIDS is a rare autosomal recessive genetic disorder 
characterized by congenital ichthyosis and abnormal brittle hair 
(trichothiodystrophy). Other features include photosensitivity, abnormal nails 
and multiple developmental defects affecting organs mainly derived from 
neuroectoderm. The exact prevalence of this condition is not known, but up to 
1991, clinical data of 15 cases with IBIDS were published .We report a case of 
Tay syndrome with additional features of Duane's retraction syndrome and Perthes 
disease, which have not yet been reported in literature.