Two patients with typical tuberous sclerosis complex (TSC) associated with 
cervical or dorsal-lumbar hydrosyringomielia are described for the first time. 
Syringomielic cavities are small in extension in both cases, leading to 
significant clinical symptoms as bilateral pes cavus and scoliosis in one 
patient only. So far, tuberous sclerosis had not been reported to involve 
primarily the spinal cord, and other factors directly linked to syringomiely are 
not present in both these patients.