de Morsier syndrome, or septo-optic dysplasia, is a developmental malformation 
complex characterized by optic nerve hypoplasia, dysgenesis of the septum 
pellucidum, and hypothalamic-pituitary dysfunction. (1,2) In Duane retraction 
syndrome, there is absence of the sixth nerve nucleus with congenital retraction 
of the globe and narrowing of the lid fissure in adduction, frequent abduction 
deficiency, and variable limitation to adduction of the affected eye. (3) The 
purpose of this report is to present a patient with the uncommon and previously 
unreported concurrence of both of these congenital malformation complexes, 
presumably because of a common disturbance of neuronal development.