A boy with congenital atrichia, ichthyosis follicular, keratitis, cutaneous 
infections and a huge inguinal hernia, but without deafness is reported. We 
believe it represents a new case of a rare X-linked recessive syndrome known as 
ichthyosis follicularis, alopecia, photophobia syndrome (IFAP). The differential 
diagnosis from keratitis ichthyosis deafness is discussed. The cutaneous 
infections seen in our case suggest the possibility of considering a genetic 
link between these syndromes.