Autoimmune hepatitis (AIH) is a progressive liver disease that is often 
associated with extrahepatic autoimmune disorders. Evans syndrome (ES) is a rare 
autoimmune disorder, which is characterized by immune thrombocytopenia and 
autoimmune hemolytic anemia. Association of AIH with ES is rare, especially in 
children. We report a 3-year-old female with a past medical history of ES who 
presented with jaundice and significant transaminitis due to AIH type 1. She 
required multiple treatments with steroids as well as azathioprine, intravenous 
immunoglobulin and a course of rituximab.