Dravet syndrome, or as it was called in the past 'severe myoclonic epilepsy in 
infancy', is a drug-resistant epilepsy first described by Charlotte Dravet in 
1978. Besides the well-known and well-described therapy resistance, Dravet 
syndrome dramatically impacts the development and behaviour of the affected 
children. As it is still not a curable disease, families need to be taught how 
to cope with the disorder and will require assistance from both clinical and 
non-clinical structures. At the onset of the disease, many questions arise 
regarding the diagnosis of Dravet syndrome, the severity of the illness and its 
deleterious effects, and the management of seizures, especially the long-lasting 
status epilepticus. Once the diagnosis has been established, severe convulsions, 
often unpredictable and long-lasting, are still a major worry, but developmental 
and behavioural problems also rapidly become a serious concern. Later on, nearly 
all parents will have a child who becomes an adult with special needs, requiring 
specialised attention from professionals.