Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial 
cardiac arrhythmia that is related to RYR2 or CASQ2 gene mutation. It occurs in 
patients with structurally normal heart and causes exercise-emotion-triggered 
syncope and sudden cardiac death. We experienced a case of CPVT in an 11 
year-old female patient who was admitted for sudden cardiovascular collapse. The 
initial electrocardiogram (ECG) on emergency department revealed ventricular 
fibrillation. After multiple defibrillations, sinus rhythm was restored. 
However, recurrent ventricular fibrillation occurred during insertion of 
nasogastric tube without sedation in coronary care unit. On ECG monitoring, 
bidirectional ventricular tachycardia occurred with sinus tachycardia and then 
degenerated into ventricular fibrillation. To our knowledge, there has been no 
previous case report of CPVT triggered by sinus tachycardia in Korea. Therefore, 
we report the case as well as a review of the literature.