For the first time Bernhard Marfan described the Marfan-Syndrome in 1896; it is 
a meso- and ectodermed variety with the conducting symptom of "arachnodactyly". 
Marfan-Syndrome is an autosomal dominant hereditary disorder with high 
penetrance and variable expressivity. In our opinion this case of a 41-year-old 
patient with kidney cysts and aneurysma dissecans of the arteria ascendens by 
Marfan-Syndrome was described in the literature only twice. The casuistics of 
this Marfan-Syndrome patient shows a particular rare associated 
organ-change--the kidney cysts--and illustrate the frequency of this hereditary 
disease.