Bartter syndrome is a rare hereditary (autosomal recessive) salt-losing 
tubulopathy characterized by hypokalemia, hypochloremia, metabolic alkalosis, 
and normal blood pressure with hyperreninemia, The underlying renal abnormality 
results in excessive urinary losses of sodium, chloride, and potassium. We 
report a case of a four-month-old infant with neonatal Bartter syndrome, who 
presented only with status epilepticus. To the best of our present knowledge, 
there is no reported case of Bartter syndrome who presented with status 
epilepticus.