The Turcot syndrome has been defined as the simultaneous presence of multiple 
polyposis of the colon and a malignant brain tumor. This association is supposed 
to be genetically transmitted, even though we still do not exactly know whether 
this occurs in a dominant or recessive way. The case of a 47-year-old man 
submitted to a right hemicolectomy for cancer and polyposis, following a series 
of endoscopic polypectomies and, finally, removal of left temporal glioma is 
here presented.