Creutzfeldt-Jakob disease (CJD) is presumably caused by a slow infectious 
pathogen or prion. The principal clinical features of Creutzfeldt-Jakob disease 
are dementia, pyramidal and extrapyramidal symptoms and signs, cerebellar 
dysfunction, and myoclonus. The patient rapidly deteriorates, declines to a 
vegetative state, becomes comatous, and is ultimately dead within several 
months. The authors present a case of Creutzfeldt-Jakob disease, proved by 
clinical findings, typical serial EEG, and pathologic features.