Carney's triad is a syndrome of unknown etiology, representing a combination of 
gastrointestinal stromal tumors, bronchial chondromas and vagal, adrenal or 
paraadrenal paragangliomas. Two of the Carney's triad components-the 
paragangliomas and the gastrointestinal stromal tumors-are potentially lethal. 
Since its first description in 1977, 79 cases have been reported so far. We 
report an 84-year-old male patient, who died of a hypertensive cerebral 
hemorrhage. Well-differentiated clear cell carcinoma of the right kidney, 
chondroma of the right bronchus and multiple jejunal stromal tumors were 
detected at autopsy. To our knowledge, this is the first report of a 
coincidental clear cell renal carcinoma in a patient with an atypical Carney's 
triad.