Ameloblastoma is an odontogenic tumor, usually benign, which rarely metastasizes 
to distant organs. The case of a 27-year-old white woman is described, who 
presented a metastatic pulmonary ameloblastoma 7 years after the removal of a 
mandibular ameloblastoma. She presented no pulmonary symptoms, but a lung nodule 
was found in a chest x-ray during a routine check-up for job admission. Computed 
tomography (CT) revealed a 2-cm well-defined solitary round nodule without 
calcifications, leading to the hypothesis of a metastatic tumor. Clinical and CT 
investigation confirmed no ameloblastoma recurrence in the jaw and no other 
primary tumor. The diagnosis of metastatic ameloblastoma was confirmed by 
microscopic evaluation of the pulmonary nodule.