The authors analyzed a family in which three descendants presented with 
adenocarcinoma of the colon. In two of them the presence of colonic adenomatosis 
was observed. Another family member, a 13-year-old girl, presented with Turcot 
syndrome, that is, brain tumor associated with colonic adenomatosis. The nature 
of the hereditary transmission of Turcot syndrome is hence analyzed, discussing 
whether it happens through an autosomal recessive or a dominant gene. 
Undoubtedly the family has colonic adenomatosis, a disease considered of 
autosomal dominant transmission. Based on the clinical observation, the authors 
suggest that Turcot syndrome may be determined by an autosomal gene with a 
pleiotropic effect and variable expressivity.