The role of chemotherapy in the treatment of myxofibrosarcoma is unclear. There 
are no randomized clinical trials evaluating the therapeutic effect of 
chemotherapy on myxofibrosarcoma. We report, to the best of our knowledge, the 
first case of myxofibrosarcoma successfully treated with mesna, pirarubicin, 
ifosfamide and dacarbazine (modified MAID) regimen. The patient achieved 
complete remission evaluated according to Response Evaluation Criteria in Solid 
Tumours (RECIST).