A 62-year-old woman with Sjogren syndrome was admitted for computed tomographic 
(CT) evaluation of a thickened trachea and parotid tumor. She had been given a 
diagnosis of mucosa-associated lymphoid tissue (MALT) lymphoma 6 years 
previously, and had undergone surgical resection of the parotid tumor. 
Endoscopic examination revealed an annular tumor that had formed a stricture in 
the mid-trachea. Pathologic specimens were obtained by surgical resection of the 
parotid tumor and bronchoscopic biopsy of the tracheal tumor. Both histological 
examinations revealed MALT-type marginal zone B-cell lymphoma. Because CD20 
immunostaining was positive, the patient received 6 cycles of rituximab plus 
cyclophosphamide, doxorubicin, vincristine, and prednisolone (CHOP) without any 
signs of major toxicity. All lesions disappeared after treatment, and this 
patient remained disease-free for 40 months.