INTRODUCTION: Carney's triad is a rare pathogenic entity which consists of the 
association in young women of multiple condromatosis in the lung, gastric 
leiomyosarcoma, and extradrenal paraganglioma; although the presence of three at 
the same time is not required for its diagnosis.
CASE REPORT: We present the case of a 27-year-old woman who was diagnosed of 
pulmonary multiple hamartomatosis and gastric stromal tumor.
DISCUSSION: A review of the literature shows the most important prognosis 
factors and therapeutic options. Surgery for gastrointestinal stromal tumors and 
extradrenal paraganglioma seems to be the best treatment up to date.