Ameloblastoma is a benign locally invasive odontogenic tumor. It is the most 
common odontogenic tumor [1]. Usually, in the middle-aged population, it is more 
common in the mandible with about 5-20% occurring in the maxilla. We report a 
case of maxillary unicystic ameloblastoma in a 3.5-year-old girl. Which 
presented clinically as a large facial swelling causing severe facial 
deformation and pressure symptoms on the left eye. CT scan showed that the 
swelling extended to involve the orbital floor. The lesion was diagnosed and 
confirmed by incisional biopsy then was successfully managed by maxillectomy and 
immediate reconstruction using the buccal pad of fat. One year follow up with no 
further complaints and no recurrence was observed. "Written informed consent was 
obtained from the patient guardians for publication of this case report and 
accompanying images. A copy of the written consent is available for review by 
the Editor-in-Chief of this journal on request".