The Meier-Gorlin syndrome (MGS) or ear, patella, short stature syndrome (MIM 
#224690) is a rare disorder with bilateral microtia, aplasia or hypoplasia of 
the patellae and severe intra-uterine and post-natal growth retardation. We 
report the case of a 10-year-old male with MGS diagnosis, his parents were 
related, he also showed conductive hearing loss and maloclussion and long upper 
central incisors, more importantly he had asymmetry of the left cerebral 
hemisphere and ventricular system, his intelligence was normal. As far as we 
know, these abnormalities have not been previously described in patients with 
MGS and the present report corresponds to the first Mexican case described so 
far.