People with rare hypertrichosis syndromes became crowd-drawing money-making 
phenomena in many 19th century sideshow acts. These individuals have been 
referred to as dog-men, hair-men, and werewolves. In 1993, Baumister et al. 
described congenital hypertrichosis lanuginose or Ambras syndrome: a distinct 
form of congenital hypertrichosis characterized by excessive hair growth over 
the body and face associated with facial and occasional dental anomalies. Much 
is not known about this syndrome since fewer than 50 cases have been documented 
worldwide. In this case report, a nine year old girl presented with excessive 
hair growth throughout her body that was denser along her midline. Furthermore, 
her face displayed the typical dysmorphic features characteristic of Ambras 
syndrome: a round tip nose, thickened nasal cartilage, antiverted nares, 
prominent philtrum with deep groove, and a trapezoid mouth. Oral examination 
revealed normal oral mucosa with completely missing and unerupted decidious and 
permanent teeth. Panoramic radiographs confirmed unerupted deciduous teeth. 
Previous case reports have mentioned the presence of occasional dental anomalies 
such as retarded first and second dentition and absence of some teeth. However, 
this is the first reported case of Ambras syndrome presenting with complete 
anodontia. Prior cytogenetic studies performed on persons with Ambras syndrome 
have implicated a balanced pericentric inversion of chromosome 8. However, it is 
likely that dental anomalies are likely a result of a different genetic 
rearrangement. Further studies are needed to explore the cause of this rare 
phenotype of Ambras syndrome with complete unerupted dentition.