Pseudotumor cerebri is an unusual syndrome of increased intracranial pressure 
without a space-occupying mass. Many associations are known, but the 
pathogenesis remains a mystery. The diagnosis and treatment of pseudotumor 
cerebri are often challenging. Because it is not rare, neurosurgeons, 
neurologists, and ophthalmologists frequently work in concert to manage these 
patients. This article reviews the diagnostic criteria and differential 
diagnosis of pseudotumor cerebri. The medical and surgical treatments currently 
employed in this disorder are discussed.