Known as D trisomy, Patau syndrome is the third chromosomopathy according to 
frequency. One of the 5000 newborn carries the trisomy 13. In over 80% cases 
there is fresh mutation with non separation in myeosis of older mother. The 
mosaic or translocation forms are not rare. The mail newborn with Patau syndrome 
is shown in this article. We notice: microcephalia, dolihocephalia, 
microphthalmia, cheilognatopalatoshisis, polydactilia, and found ultrasound 
changes at the brain, hearth and genitourinary system. Cytogenetic finding show: 
mail cariotype with aberrations 47, XY + 13, Sy Patau.