Recently, several genes for parkinsonism have been identified. Among them, 
familial Parkinson's disease (PD) could be assigned for PARK disorders. PARK 
disorders consist of three different inherited modes such as autosomal 
recessive, autosomal dominant modes and susceptible genes. Some of them manifest 
not only typical parkinsonism, but also dystonia, pyramidal sign, and mental 
dysfunctions. While the monogenic forms of PARK disorders have been reviewed 
extensively, it is not easy to do differential diagnosis of PARK disorders due 
to the additional features except for typical parkinsonism. In this 
presentation, we focus on two different scenarios of patients with autosomal 
dominant parkinsonism: (1) parkinsonism with mutations in one of the PARK genes; 
(2) parkinsonism with mutations other than PARK genes or yet other genes where 
parkinsonism is a well recognized, concomitant, or even an isolated feature.