Aortitis is the all-encompassing pathological term ascribed to inflammation of 
the aorta. Regardless of the etiology, it frequently results in aortic root 
dilatation and aortic insufficiency rather than aortic stenosis. The rare case 
of aortitis such as isolated idiopathic aortitis may occur without evidence of 
systenic inflammatory disease or infection, and usually has subclinical nature. 
Even though the goals of therapy include immediate treatment of aortic 
inflammation or infection, the optimal management of isolated idiopathic 
aortitis is uncertain. We report a rare case of isolated idiopathic aortitis 
mimicking acute severe aortic stenosis, which was improved after steroid 
therapy.