Tracheobronchial cartilage calcification is a rare finding in the pediatric 
population. Keutel syndrome (OMIM 245150) is a very rare syndrome characterized 
with diffuse calcification of cartilage, brachytelephalangia, pulmonary 
stenosis, midline defects, stippled epiphysis in infancy, and hearing loss 
accompanied by recurrent respiratory infections and asthma-like attacks. Here, 
we present a 14-year-old patient who was followed up with the diagnosis of 
asthma, but did not respond to appropriate asthma treatment. She was 
subsequently diagnosed as having Keutel syndrome with cartilage calcification on 
the tracheobranchial tree and auricula, atypical facial features, recurrent 
otitis media, hearing loss, and recurrent asthma-like symptoms.